“Prion based diseases are 100% fatal.”
Yes, the misfolded protein is simply incompatible with life.
And the instant Internet epidemiologists on this thread poo-pooing the threat miss the wonderful potential for this to become transmissible via aerosol.
Odd that something so small could be so destructive.
Re: 70 - aerosol? I find that unlikely unless perhaps a cervid sneezed in your face - repeatedly.
I would assess the risk of infection of contracting TSE from a cervid that has CWD as low. I don’t wallow in gut pits, or dress deer without gloves. Common steps to reduce exposure.